problendoПроблемы ЭндокринологииProblems of Endocrinology0375-96602308-1430Endocrinology Research Centre10.14341/probl201460251-67problendo-6930Research ArticleСтатьиArticlesФедеральные клинические рекомендации по диагностике и лечению адренокортикального ракаFederal clinical practice guidelines on the diagnostics and treatment of adrenocortical cancerМельниченкоГ АMelnichenkoG A-СтилидиИ СStilidiI S-АлексеевБ ЯAlekseevB Ya-ГорбуноваВ АGorbunovaV A-БельцевичД ГBeltsevichD Gbeltsevich@rambler.ruРайхманА ОRaikhmanA O-КузнецовН СKuznetsovN S-ЖуковН ВZhukovN V-БохянВ ЮBokhyanV Yu-ГБОУ ВПО «Первый московский государственный университет им. И.М. Сеченова» Минздрава России, МоскваEndocrinology Research Centre, Moscow; Sechenov First Moscow State Medical Univesity, MoscowФГБУ «Российский онкологический научный центр им. Н.Н. Блохина» РАМН, МоскваN.N. Blokhin Russian Cancer Research Center of the Russian Academy of Medical Sciences, MoscowФГБУ «Московский научно-исследовательский онкологический институт им. П.А. Герцена» Минздрава РоссииP.A. Hertsen Moscow Cancer Research Institute, MoscowФГБУ «Эндокринологический научный центр» Минздрава России, МоскваEndocrinology Research Centre, MoscowГБОУ ВПО «Первый московский государственный университет им. И.М. Сеченова» Минздрава России, МоскваSechenov First Moscow State Medical Univesity, MoscowФГБУ «Московский научно-исследовательский онкологический институт им. П.А. Герцена» Минздрава России; ФГБУ «ФНКЦ детской гематологии, онкологии и иммунологии им. Д. Рогачева» Минздрава России, МоскваP.A. Hertsen Moscow Cancer Research Institute, Moscow; Federal Scientific Clinical Centre of Pediatric Hematology Oncology Immunology named after Dmitry Rogachev, Moscow201415042014602ТОМ 60, №2 (2014)5167Copyright © Мельниченко Г.А., Стилиди И.С., Алексеев Б.Я., Горбунова В.А., Бельцевич Д.Г., Райхман А.О., Кузнецов Н.С., Жуков Н.В., Бохян В.Ю., 20142014Мельниченко Г.А., Стилиди И.С., Алексеев Б.Я., Горбунова В.А., Бельцевич Д.Г., Райхман А.О., Кузнецов Н.С., Жуков Н.В., Бохян В.Ю.Melnichenko G.A., Stilidi I.S., Alekseev B.Y., Gorbunova V.A., Beltsevich D.G., Raikhman A.O., Kuznetsov N.S., Zhukov N.V., Bokhyan V.Y.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.probl-endojournals.ru/jour/article/view/6930

Определение гормональной активности и злокачественного потенциала - актуальнейший вопрос диагностики и выбора лечебной тактики при опухолях надпочечников. Адренокортикальный рак (АКР) - достаточно редкое заболевание, которое характеризуется плохими прогностическими показателями. Встречаемость АКР 0,5-2 случая на миллион населения, в структуре инциденталом надпочечников не более чем в 2-4% наблюдений. Для широкого обсуждения предлагается проект клинических рекомендаций по диагностике и лечению АКР, предназначенного для онкологов, хирургов, эндокринологов, специалистов по лучевой диагностике, патоморфологов и др.

Statement of hormonal activity and potential malignancy are the most important issues of diagnosis and selection of appropriate treatment way for patients with adrenal tumors. Adrenal cortical carcinoma (ACC) is rare disease with poor prognosis. Incidience of ACC is about 0.5-2 per million, and no more then 2-4% among adrenal tumors. This draft of guidelines of diagnosis and treatment of ACC is offered to common discussion among wide round of specialists.

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The authors declare that there are no conflicts of interest present.