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Болезнь фон Гиппеля-Линдау (VHL-синдром)

https://doi.org/10.14341/probl201258234-41

Аннотация

Болезнь фон Гиппеля-Линдау является наследственным опухолевым синдромом, предполагающим развитие различных доброкачественных и злокачественных новообразований (гемангиобластома центральной нервной системы и сетчатки глаза, опухоль внутреннего уха, карцинома и кисты почек, феохромоцитома, нейроэндокринная опухоль и кисты поджелудочной железы, цистаденома придатка яичка у мужчин и широкой связки у женщин). Болезнь фон Гиппеля-Линдау - наиболее распространенная причина наследственного рака почки.

Список литературы

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Для цитирования:


., ., ., . Болезнь фон Гиппеля-Линдау (VHL-синдром). Проблемы Эндокринологии. 2012;58(2):34-41. https://doi.org/10.14341/probl201258234-41

For citation:


Iukina M.I., Tiul'pakov A.N., Troshina E.A., Bel'tsevich D.G. Von Hippel-Lindau disease (VHL-syndrome). Problems of Endocrinology. 2012;58(2):34-41. (In Russ.) https://doi.org/10.14341/probl201258234-41

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