Множественная эндокринная неоплазия 2-го типа


Наследственная форма феохромоцитомы отличается склонностью к рецидиву, двустороннему, мультицентричному и первично-множественному поражению. Для пациентов с синдромом множественных эндокринных неоплазий 2-го типа не характерны вненадпочечниковая локализация феохромоцитомы и наличие метастазов. Обследование и лечение данной категории пациентов необходимо проводить с учетом этих особенностей. На примере семьи с синдромом множественных эндокринных неоплазий 2-го типа освещены вопросы ведения пациентов с генетически-детерминированной феохромоцитомой.

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Для цитирования:

., ., ., . Множественная эндокринная неоплазия 2-го типа. Проблемы Эндокринологии. 2011;57(6):21-26.

For citation:

Iukina M.I., Goncharov N.P., Bel'tsevich D.G., Troshina E.A. Multiple type 2 endocrine neoplasia (case report). Problems of Endocrinology. 2011;57(6):21-26. (In Russ.)

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