Проблемы Эндокринологии

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Карни-комплекс - синдром множественных эндокринных неоплазий


Карни-комплекс - редкий наследственный синдром с аутосомно-доминантным типом наследования, характеризующийся множественными неоплазиями, в том числе органов эндокринной системы. Типичными проявлениями этого синдрома являются микронодулярная пигментная дисплазия надпочечников, лентигиноз, миксомы сердца и кожи, крупноклеточные сертолиомы, а также ряд других неоплазий. На сегодняшний день в мире описано всего несколько сотен таких пациентов. Представлен обзор современных сведений о Карни-комплексе.

Об авторах

E Orlova

M Kareva

Список литературы

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Для цитирования:

., . Карни-комплекс - синдром множественных эндокринных неоплазий. Проблемы Эндокринологии. 2012;58(3):22-30.

For citation:

Orlova E.M., Kareva M.A. Carney complex - multiple endocrine neoplasia syndrome. Problems of Endocrinology. 2012;58(3):22-30. (In Russ.)

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ISSN 0375-9660 (Print)
ISSN 2308-1430 (Online)