Clinical variants of McCune-Albright-Braitsev syndrome in girls
https://doi.org/10.14341/probl11560
Abstract
The authors analyze published data on clinical variants and hormonal parameters in patients with this syndrome and present their own observations of children with this condition. Besides early sexual maturation, they describe the clinical picture of Cushing’s syndrome, thyroid nodular hyperplasia. The said disorders do not depend on the tropic effect of the hypothalamohypophyseal system. A hypothesis is put forward about primary activation of adenylate cyclase system in the origin of the disease.
About the Authors
T V SemichevaEndocrinology Research Centre
Russian Federation
Ye B Koledova
Endocrinology Research Centre
Russian Federation
E S Kuznetsova
Endocrinology Research Centre
Russian Federation
A D Dobracheva
Endocrinology Research Centre
Russian Federation
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Review
For citations:
Semicheva T.V., Koledova Ye.B., Kuznetsova E.S., Dobracheva A.D. Clinical variants of McCune-Albright-Braitsev syndrome in girls. Problems of Endocrinology. 1994;40(2):44-46. (In Russ.) https://doi.org/10.14341/probl11560

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