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Clinical variants of McCune-Albright-Braitsev syndrome in girls

https://doi.org/10.14341/probl11560

Abstract

The authors analyze published data on clinical variants and hormonal parameters in patients with this syndrome and present their own observations of children with this condition. Besides early sexual maturation, they describe the clinical picture of Cushing’s syndrome, thyroid nodular hyperplasia. The said disorders do not depend on the tropic effect of the hypothalamohypophyseal system. A hypothesis is put forward about primary activation of adenylate cyclase system in the origin of the disease.

About the Authors

T V Semicheva

Endocrinology Research Centre


Russian Federation


Ye B Koledova

Endocrinology Research Centre


Russian Federation


E S Kuznetsova

Endocrinology Research Centre


Russian Federation


A D Dobracheva

Endocrinology Research Centre


Russian Federation


References

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Review

For citations:


Semicheva T.V., Koledova Ye.B., Kuznetsova E.S., Dobracheva A.D. Clinical variants of McCune-Albright-Braitsev syndrome in girls. Problems of Endocrinology. 1994;40(2):44-46. (In Russ.) https://doi.org/10.14341/probl11560

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ISSN 0375-9660 (Print)
ISSN 2308-1430 (Online)